Common pulmonary vein atresia: Report of three cases and review of the literature

Authors

Michael Perez, University of Tennessee Health Science Center
T. K.Susheel Kumar, University of Tennessee Health Science Center
Mario Briceno-Medina, University of Tennessee Health Science Center
Mohammed Alsheikh-Ali, University of Tennessee Health Science Center
Shyam Sathanandam, University of Tennessee Health Science Center
Christopher J. Knott-Craig, University of Tennessee Health Science Center

Abstract

Common pulmonary vein atresia is a rare and usually fatal congenital anomaly, in which the pulmonary veins come together to form a confluence that does not connect to the left atrium. We report our experience with three cases of common pulmonary vein atresia and review the literature on this anomaly. The diagnosis of common pulmonary vein atresia must be entertained in any newborn that presents with cyanosis, refractory acidosis, and decreased systemic perfusion within the first 48 hours of life. Echocardiography is a useful screening tool, but cardiac catheterisation is the preferred diagnostic tool. Common pulmonary vein atresia can be fatal without surgical intervention, but survival after surgery continues to be poor.

Publication Title

Cardiology in the Young

Recommended Citation

Perez, M., Kumar, T., Briceno-Medina, M., Alsheikh-Ali, M., Sathanandam, S., & Knott-Craig, C. (2016). Common pulmonary vein atresia: Report of three cases and review of the literature. Cardiology in the Young, 26 (4), 629-635. https://doi.org/10.1017/S1047951115002334